Korean J Otolaryngol-Head Neck Surg.  2005 Jun;48(6):819-822.

Nevoid Basal Cell Carcinoma Syndrome: A Case Report and Literature Review

Affiliations
  • 1Department of Otorhinolaryngology-Head and Neck Surgery, Eul-Ji University College of Medicine, Daejeon, Korea. otalgia@naver.com

Abstract

Nevoid basal cell carcinoma syndrome (NBCCS), also known as Gorlin-Goltz syndrome, shows autosomal dominant pattern of inheritance with variable expressivity. The most important features are the occurrence of basal cell carcinoma and odontogenic keratosis. Recently, we experienced a case of nevoid basal cell carcinoma syndrome with multiple odontogenic keratocysts, basal cell carcinoma on cheek, cerebral calcification and palmar pits. We report this case with literature review.

Keyword

Nevoid basal cell carcinoma syndrome; Odontogenic keratocyst

MeSH Terms

Basal Cell Nevus Syndrome*
Carcinoma, Basal Cell
Cheek
Keratosis
Odontogenic Cysts
Wills
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