Korean J Otolaryngol-Head Neck Surg.
2005 Jun;48(6):819-822.
Nevoid Basal Cell Carcinoma Syndrome: A Case Report and Literature Review
- Affiliations
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- 1Department of Otorhinolaryngology-Head and Neck Surgery, Eul-Ji University College of Medicine, Daejeon, Korea. otalgia@naver.com
Abstract
- Nevoid basal cell carcinoma syndrome (NBCCS), also known as Gorlin-Goltz syndrome, shows autosomal dominant pattern of inheritance with variable expressivity. The most important features are the occurrence of basal cell carcinoma and odontogenic keratosis. Recently, we experienced a case of nevoid basal cell carcinoma syndrome with multiple odontogenic keratocysts, basal cell carcinoma on cheek, cerebral calcification and palmar pits. We report this case with literature review.