Chonnam Med J.  2007 Aug;43(2):105-109.

The Natural Course of Congenital Pulmonary Valve Stenosis

• Cho YK
• Ma JS

Abstract

Aa s rule, mild pulmonary valvular stenosis (PVS) is not treated, as it goes not progress. We retrospectively evaluated 178 patients who were diagnosed PVS by echocardiogram from January 2001 through December 2005 at the Department of Pediatrics, Chonnam National University Hospital. The age at initial diagnosis ranged from 1 day to 22 years. The combined cardiac anomaly are patent foramen ovale (14.6%), tricuspid regurgitation (14.0%), peripheral pulmonary stenosis (3.9%), aortic valve stenosis (3.4%) and aortic regurgitation (1.7%). 120 patients had the PVS transvalvular pressure gradient (PG) below 30 mmHg. Among them, 14 were followed up. Their mean PG at diagnosis was 20.4+/-6.0 mmHg and follow-up was 19.4+/-7.5 mmHg. 33 patients had the PVS PG between 30 mmHg and 50 mmHg. Among them, 7 were followed up. Their mean PG at diagnosis was 36.0+/-5.8 mmHg and follow-up was 25.7+/-12.1 mmHg, with 10.3 mmHg decrease (p<0.01). 25 patients had PVS PG above 50 mmHg. Among them, 13 were followed up. Their mean transvalvular PG at diagnosis was 66.3+/-15.8 mmHg and at follow-up was 65.1+/-27.9 mmHg. In conclusion, the patients with PAS PG between 30 and 50 mmHg must be followed by regularly, while those with PG above 50 mmHg must be treated according to their signs or symptoms.

Keyword

Pulmonary valvular stenosis; Natural course

MeSH Terms

Aortic Valve Insufficiency
Aortic Valve Stenosis
Constriction, Pathologic
Diagnosis
Follow-Up Studies
Foramen Ovale, Patent
Humans
Jeollanam-do
Pediatrics
Pulmonary Valve Stenosis*
Pulmonary Valve*
Retrospective Studies
Tricuspid Valve Insufficiency