Korean J Obstet Gynecol.  2009 Jul;52(7):781-785.

Diagnosis and treatment of uterine didelphys with obstructed hemivagina and ipsilateral renal agenesis

• Park JS
• Ahn ST
• Kim MR
• Hwang KJ

Abstract

Uterine malformations consist of a group of miscellaneous congenital anomalies of the female genital system, and these anomalies are the result of major disturbances in the development, such as formation or fusion of the Mullerian or paramesonephric ducts during fetal life. The Mullerian anomalies have been estimated to occur in up to 0.001~10%, and these anomalies may be associated with numerous congenital anomalies, and ipsilateral renal anomalies especially are the most common. The uterine didelphys with obstructed hemivagina and ipsilateral renal agenesis clinically may result in dysmenorrhea, low abdominal pain, endometriosis or pelvic mass after menarche. Furthemore the delayed diagnosis causes infertility and poor pregnancy outcome due to continued retrograde menstruation which leads to endometriosis and distorted pelvic anatomy. These anomalies could be diagnosed with ultrasonography and MRI that have the high sensitivity and specificity. Excision of vaginal septum and marsupialization are appropriate treatments to relieve symptoms and reserve fertility. We report 7 cases of uterine didelphys with obstructed hemivagina and ipsi-unilateral renal agenesis with a brief review of relevant literatures to help understand these anomalies.

Keyword

Uterine didelphys; Obstructed hemivagina; Ipsilateral renal agenesis

MeSH Terms

Abdominal Pain
Congenital Abnormalities
Delayed Diagnosis
Dysmenorrhea
Endometriosis
Female
Fertility
Humans
Infertility
Kidney
Kidney Diseases
Menarche
Menstruation Disturbances
Pregnancy
Pregnancy Outcome
Sensitivity and Specificity
Congenital Abnormalities
Kidney
Kidney Diseases