Korean J Obstet Gynecol.  2003 Jun;46(6):1213-1217.

A Case of Vulvar Paget's Disease Associated with Adenocarcinoma Occurred in Young Woman

• Choi YS
• Sol ES
• Park SY
• Lee TS

Abstract

Extramammary Pagets disease of the vulva is an uncommon vulvar neoplasm with a high rate of recurrence. We report a young woman in whom vulval Paget's disease occurred in association with local adenocarcinoma. The patient presented at the age of 28 years with slowly growing vulval mass which had some mucoid discharge. Biopsy of the mass showed Paget's disease with associated local adenocarcinoma. This patient received modified radical vulvectomy with unilateral inguinofemoral lymphadenectomy. Until now she is under follow up without evidence of recurrence for 24 months. According to our medline research from 1980 to 2000, this case is the youngest asian patient yet recorded. We recommend that abnormally growing vulvar mass need to be biopsied eventhough she is young.

Keyword

Paget's disease; Extramammary; Paget's disease of the vulva; Adenocarcinoma

MeSH Terms

Adenocarcinoma*
Asian Continental Ancestry Group
Biopsy
Female
Follow-Up Studies
Humans
Lymph Node Excision
Paget Disease, Extramammary
Recurrence
Vulva
Vulvar Neoplasms