Korean J Med.  2015 Jan;88(1):69-73. 10.3904/kjm.2015.88.1.69.

Isolated Right Ventricular Noncompaction Accompanied by Right Ventricular Failure

Affiliations
  • 1Department of Internal Medicine, Soonchunhyang University Cheonan Hospital, Soonchunhyang University College of Medicine, Cheonan, Korea.
  • 2Department of Internal Medicine, Soonchunhyang University Gumi Hospital, Soonchunhyang University College of Medicine, Cheonan, Korea. jichoona@gmail.com

Abstract

Noncompaction of the ventricular myocardium is a rare congenital cardiomyopathy caused by arrest of normal endomyocardial embryogenesis. Isolated right ventricular noncompaction (IRNC) is an even rarer form of this disease. We report herein on a 68 year-old male diagnosed with IRNC who presented with right-sided heart failure, without involvement of the left ventricle. Diagnosis was achieved with the aid of echocardiography and ventriculography. Medical treatment including prescription of diuretics, a calcium channel blocker, and digitalis, improved both the symptoms and right ventricular function.

Keyword

Right ventricular noncompaction; Echocardiography; Right-sided heart failure

MeSH Terms

Calcium Channels
Cardiomyopathies
Diagnosis
Digitalis
Diuretics
Echocardiography
Embryonic Development
Female
Heart Failure
Heart Ventricles
Humans
Male
Myocardium
Pregnancy
Prescriptions
Ventricular Function, Right
Calcium Channels
Diuretics
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