Korean J Med.  2015 Apr;88(4):480-485. 10.3904/kjm.2015.88.4.480.

Pneumatosis Cystoides Intestinalis in a Patient with Dermatomyositis: A Case Report and Review of the Literature

• Yu MY
• Lee KL
• Park JK
• Ahn GY
• Son CN
• Cho OK
• Jun JB

• KMID: 2269138
• DOI: http://doi.org/10.3904/kjm.2015.88.4.480

Abstract

Pneumatosis cystoides intestinalis (PCI) is a rare disease with intramural gas formation in the gastrointestinal tract. The causes of PCI are various, and are commonly associated with collagen vascular disease. We present a case of a 48-year-old female with dermatomyositis (DM) who also developed PCI. Her risk of PCI may have been increased by multiple factors such as gender, DM itself, and medications including corticosteroids, methotrexate, and azathioprine. While the cause of, and risk factors for PCI in DM patients are not well known on a global scale, outcomes range from benign to life threatening. Therefore, we present a case study and review the literature to identify candidate risk factors for PCI.

Keyword

Pneumatosis cystoides intestinalis; Dermatomyositis

MeSH Terms

Adrenal Cortex Hormones
Azathioprine
Collagen
Dermatomyositis*
Female
Gastrointestinal Tract
Humans
Methotrexate
Middle Aged
Pneumatosis Cystoides Intestinalis*
Rare Diseases
Risk Factors
Vascular Diseases
Adrenal Cortex Hormones
Azathioprine
Collagen
Methotrexate