Korean J Obstet Gynecol.  1998 Aug;41(8):2246-2250.

Two Cases of Prenatal Diagnosis of Congenital Cystic Adenomatoid Malformation of the Lung

• Kim JH
• Yang GH
• Bang HM
• Jung MJ
• Jin SJ

Abstract

Congenital cystic adenomatoid malformation (CCAM) is a rare pulmonary lesion that can be diagnosed prenatally by ultrasonography. CCAM is a benign hamartomatous or dysplastic tumor that is characterized by overgrowth of the terminal bronchioles. It is typically unilateral and usually involves one lobe or segment with a broad spectrum of clinical presentation. In 1977, Stocker et al. examined 38 cases of CCAM and divided these lesions into three types based on the gross size of the cysts and histologic findings. The overall prognosis of an affected fetus depends on the size of the lung mass and the secondary pathophysiologic derangement. Recently we experienced two cases of congenital cystic adenomatoid malformation of the lung, which was diagnosed by prenatal ultrasonography.

Keyword

Congenital cystic adenomatoid malformation ( CCAM ); Fetal hydrops; Hydramnios

MeSH Terms

Bronchioles
Cystic Adenomatoid Malformation of Lung, Congenital*
Fetus
Hydrops Fetalis
Lung*
Polyhydramnios
Prenatal Diagnosis*
Prognosis
Ultrasonography
Ultrasonography, Prenatal