Korean J Med.  2010 Aug;79(2):206-209.

A case of angioimmunoblastic T cell lymphoma in a patient with ichthyosis

• Lee SH
• Lee JM
• Beom SH
• Hong SH
• Oh SY

Abstract

Angioimmunoblastic T cell lymphoma (AITL), which accounts for only 1~2% of non-Hodgkin's lymphomas, is commonly accompanied by skin lesions. Those associated with AITL include erythematous plaques, nodules or rashes. Histological examination of most lesions shows infiltration by malignant lymphocytes. Ichthyosis is a generalized skin disease characterized by hyperkeratosis, in which the skin acquires an appearance resembling fish scales. Some cases may be acquired, but most have a genetic basis. We report a case of AITL with associated ichthyosis that is considered to be inherited.

Keyword

Angioimmunoblastic T cell lymphoma; Immunoblastic lymphadenopathy; Ichthyosis

MeSH Terms

Exanthema
Humans
Ichthyosis
Immunoblastic Lymphadenopathy
Lymphocytes
Lymphoma, Non-Hodgkin
Lymphoma, T-Cell
Skin
Skin Diseases
Weights and Measures