Korean J Med.  2006 Jul;71(1):80-85.

Partial agenesis of dorsal pancreas with Castleman's disease in pancreatic tail area

Affiliations
  • 1Department of Internal Medicine, Yonsei University College of Medicine, Seoul, Korea. sysong@yumc.yonsei.ac.kr
  • 2Department of General Surgery, and Institute of Gastroenterology, Yonsei University College of Medicine, Seoul, Korea.

Abstract

Agenesis of dorsal pancreas is a very rare congenital anomaly which comes from the failure of development of the body and tail of pancreas in embryogenesis. Castleman's disease is a rare lymphoid tumor which usually occurred in the mediastinum, but it is very uncommon in the retroperitoneal pancreatic tail area. We report a case of partial agenesis of dorsal pancreas with Castleman's disease in pancreatic tail area, mimicking a pancreatic tumor. A 46-year-old woman was admitted to our hospital with intermittent abdominal discomfort for 2 months. Computed tomography, magnetic resonance imaging, and endoscopic retrograde cholangiopancreatography (ERCP) revealed a tumor at distal pancreatic tail area, short pancreatic duct, and absence of pancreatic body and tail. The surgical excision of the tumor revealed hyaline-vascular type Castleman's disease.

Keyword

Castleman's disease; Agenesis; Pancreas

MeSH Terms

Cholangiopancreatography, Endoscopic Retrograde
Embryonic Development
Female
Giant Lymph Node Hyperplasia*
Humans
Magnetic Resonance Imaging
Mediastinum
Middle Aged
Pancreas*
Pancreatic Ducts
Pregnancy
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