Korean J Cerebrovasc Surg.  2005 Sep;7(3):241-244.

Hemichoreoathetosis as an Initial Manifestation of Moyamoya Disease: A Case Report

Affiliations
  • 1Department of Neurosurgery, School of Medicine, Pusan National University, Busan, Korea. md@medimail.co.kr

Abstract

We report a case of moyamoya disease in a 7-year-old boy whose initial manifestation was the sudden onset of right hemichoreoathetosis for one week. Magnetic resonance imaging demonstrated a small infarction in the left frontal subcortical white matter. Single photon emission computed tomography (SPECT) revealed a perfusion defect in the same region. Combined superficial temporal artery-middle cerebral artery (STA-MCA) anastomosis and encephalo-duro-arterio-myo-synangiosis (EDAMS) were performed and his symptoms disappeared after surgery. SPECT also normalized after revascularization. Hemichoreoathetosis is a rare initial manifestation of moyamoya disaese and direct and indirect anastomosis is effective treatment of this rare symptom.

Keyword

Moyamoya disease; Hemichoreoathetosis; Revascularization

MeSH Terms

Cerebral Arteries
Child
Humans
Infarction
Magnetic Resonance Imaging
Male
Moyamoya Disease*
Perfusion
Tomography, Emission-Computed, Single-Photon
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