Korean J Cerebrovasc Surg.
2005 Sep;7(3):241-244.
Hemichoreoathetosis as an Initial Manifestation of Moyamoya Disease: A Case Report
- Affiliations
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- 1Department of Neurosurgery, School of Medicine, Pusan National University, Busan, Korea. md@medimail.co.kr
Abstract
- We report a case of moyamoya disease in a 7-year-old boy whose initial manifestation was the sudden onset of right hemichoreoathetosis for one week. Magnetic resonance imaging demonstrated a small infarction in the left frontal subcortical white matter. Single photon emission computed tomography (SPECT) revealed a perfusion defect in the same region. Combined superficial temporal artery-middle cerebral artery (STA-MCA) anastomosis and encephalo-duro-arterio-myo-synangiosis (EDAMS) were performed and his symptoms disappeared after surgery. SPECT also normalized after revascularization. Hemichoreoathetosis is a rare initial manifestation of moyamoya disaese and direct and indirect anastomosis is effective treatment of this rare symptom.