Korean J Nephrol.
2010 Jul;29(4):513-518.
Recurrent Systemic Capillary Leak Syndrome Responding to the Corticosteroid Therapy
- Affiliations
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- 1Department of Nephrology, Korea University Medical College Ansan Hospital, Korea. starch70@korea.ac.kr
- 2Department of Pathology, Korea University Medical College Ansan Hospital, Korea.
Abstract
- Systemic capillary leak syndrome (SCLS) is a rare devastating condition that is caused by unexplained marked capillary hyperpermeability, resulting in hypovolemic shock, hemoconcentration, and hypoproteinemia. Most patients have prodromal symptoms such as non-specific gastrointestinal symptoms, myalgia, or dizziness. In the current case, we observed the patient with recurrent SCLS show perivascular lymphocytic infiltration on skin biopsy and eosinophilic infiltrates on random biopsies from duodenum to colon. This finding might be due to distinct eosinophilic enterocolitis or secondary to SCLS. However, there has been rare data for the prevention of the recurrent attack of SCLS, although the mortality is high. Therefore, we report a case of frequently relapsing SCLS responding to the corticosteroid therapy.
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