Korean J Dermatol.  2002 Jun;40(6):682-685.

A Case of Nevoid Basal Cell Carcinoma Syndrome with Multiple, Symmetrically Distributed Basal Cell Carcinomas

• Tak WJ
• Shin BJ
• Kim MN
• Ro BI

Abstract

Nevoid basal cell carcinoma syndrome is a rare inherited disorder characterized by multiple cutaneous basal cell carcinoma, pits of the palms and soles, cysts of the jaws, and ectopic calcification of cranial membranes. The patient was a 66 year old female. She complained of multiple, symmetrically distributed black-colored papules on the both sides of the neck. On physical examination, multiple pits were detected in the palms and soles. The histopathologic findings of the papules showed variable shaped and sized tumor nests composed of basaloma cells. On PNS CT for search of metastasis of the cancer, odontogenic keratocyst was detected at the Lt. alveolar process of maxilla by accident. We diagnosed her nevoid basal cell carcinoma syndrome and the lesions on both sides of the neck were removed completely.

Keyword

Nevoid basal cell carcinoma syndrome; Basal cell carcinoma; Pits of palms and soles; Odontogenic kertocyst

MeSH Terms

Aged
Alveolar Process
Basal Cell Nevus Syndrome*
Carcinoma, Basal Cell*
Female
Humans
Jaw
Maxilla
Membranes
Neck
Neoplasm Metastasis
Odontogenic Cysts
Physical Examination