Korean J Dermatol.  2008 Nov;46(11):1538-1542.

A Case of Progressive Facial Hemiatrophy

Affiliations
  • 1Department of Dermatology, School of Medicine, Gyeongsang National University and Gyeongsang Instiute of Health Science, Jinju, Korea. deroh@nongae.gsnu.ac.kr

Abstract

Progressive facial hemiatrophy (PFH) was first described by Parry and Romberg and this is a rare disorder of an unknown origin. PFH is characterized by slowly progressive, mostly unilateral facial atrophy of the skin, soft tissues, muscles and underlying bony structures and is usually develops in the first or second decade of life. Although the clinical presentation of PFH may appear similar to localized linear scleroderma en coup the sabre, some patients presenting with PFH have neither en coup the sabre nor generalized sclerosis. Herein, we report on an unusual case of a 7-year-old girl who presented with progressive hemiatrophy of the face.

Keyword

Progressive facial hemiatrophy; Scleroderma en coup de sabre

MeSH Terms

Atrophy
Child
Facial Hemiatrophy
Humans
Muscles
Scleroderma, Localized
Sclerosis
Skin
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