Korean J Hepatobiliary Pancreat Surg.  1999 Aug;3(2):163-167.

Cavernous Transformation of Portal Vein with Right Lobe Hypoplasia of Liver: A Case Report

• Chung CW
• Kang CM
• Choi JS
• Kim BR

Abstract

Cavernous transformation of the portal vein that is resulted as a collateral vessel formation from a portal hypoplasia is very rarely to be observed in human being. Such an abnormal transformation can be caused by congenital defect of vein formation in the early embryonal development or congenital hematologic hypercoagulability which gives rise to the cavernous development of cavernous collateral branches. Acute thrombosis of portal vein can also be the cause of acquired cavernous transformation. In most cases it extends into the parenchyme of liver, and often has porto-systemic shunt (with left gastropiploic vein and varices around spleen) or porto-portal shunt (with varices around gallbladder). A 48 years old male patient underwent splenectomy at the age of 24 owing to splenomegaly. He had liver cirrhosis without hepatitis and alcohol history. Intrahepatic stone in left lateral lobe of liver was diagnosed in the course of medical treatment. The cavernous transformation of portal vein with right lobe hypoplasia was confrimed during the operation.

MeSH Terms

Congenital Abnormalities
Hepatitis
Humans
Liver Cirrhosis
Liver*
Male
Middle Aged
Portal Vein*
Splenectomy
Splenomegaly
Thrombophilia
Thrombosis
Varicose Veins
Veins