Korean J Anesthesiol.  2008 Nov;55(5):639-643. 10.4097/kjae.2008.55.5.639.

Anesthesiologic considerations in a pediatric patient with cornelia de lange syndrome: A case report

• Ro J
• Kim EJ
• Lee JH
• Min BW
• Lee SG
• Ban JS

• KMID: 2243010
• DOI: http://doi.org/10.4097/kjae.2008.55.5.639

Abstract

Cornelia de Lange syndrome (CdLS) is a relatively uncommon, multiple malformation syndrome involving neurodevelopmental, craniofacial, cardiac, musculoskeletal and gastrointestinal systems. Anesthetic management of a patient with CdLS may pose a serious problem mainly from difficult tracheal intubation, aspiration complications and cardiac malformation. We report our successful experience in anesthetic management of a 15-month-old male patient with CdLS who underwent orchiopexy for bilateral cryptochidism.

Keyword

aspiration complications; cardiac malformation; Cornelia de Lange syndrome; difficult tracheal intubation

MeSH Terms

De Lange Syndrome
Humans
Infant
Intubation
Male
Orchiopexy