Korean J Anesthesiol.  2006 Jul;51(1):120-123. 10.4097/kjae.2006.51.1.120.

Anesthetic Management of a Patient with Noonan Syndrome: A case report

• Kim MS
• Cho JE
• Kil HK

• KMID: 2239908
• DOI: http://doi.org/10.4097/kjae.2006.51.1.120

Abstract

Noonan syndrome is featured by short stature, mental retardation, facial dysmorphia, webbed neck, and heart defects. The phenotype has some similarities with Turner syndrome, but the karyotype is normal and males can be affected. We used Bonfils fiberscope for intubation because we suspected the difficult airway. We report the experience of anesthetic management for osteotomy of calcaneonavicular coalition in a patient with Noonan syndrome.

Keyword

anesthetic management; Noonan syndrome; osteotomy

MeSH Terms

Heart
Humans
Intellectual Disability
Intubation
Karyotype
Male
Neck
Noonan Syndrome*
Osteotomy
Phenotype
Turner Syndrome