Korean J Anesthesiol.  2009 Sep;57(3):376-380. 10.4097/kjae.2009.57.3.376.

Respiratory failure due to myotonic dystrophy combined with peripartum cardiomyopathy: A case report

• Shim HS
• Shin MK
• Cho JY
• Kim IK
• Lee SH

• KMID: 2236512
• DOI: http://doi.org/10.4097/kjae.2009.57.3.376

Abstract

Myotonic dystrophy is an autosomal-dominant inherited neuromuscular disorder that's characterized by slowly progressive muscular dystrophy, muscle weakness and myotonia. The clinical features may vary from just cataracts to involvement of multiple organ systems such as various muscles, the heart, lung and intestine. Its most common complication is postoperative respiratory failure. We encountered a patient who developed sudden unexpected peripartum cardiomyopathy (PPCM) and respiratory failure due to presumed myotonic dystrophy after cesarean section. We report here on our clinical experience with this malady and we include a brief review of the medical literature on myotonic dystrophy.

Keyword

Myotonic dystrophy; Peripartum cardiomyopathy; Respiratory failure

MeSH Terms

Cardiomyopathies
Cataract
Cesarean Section
Female
Heart
Humans
Intestines
Lung
Muscle Weakness
Muscles
Muscular Dystrophies
Myotonia
Myotonic Dystrophy
Peripartum Period
Pregnancy
Respiratory Insufficiency