J Rheum Dis.  2012 Apr;19(2):108-111. 10.4078/jrd.2012.19.2.108.

A Case of Cortical Vein Thrombosis in Wegener's Granulomatosis

• Choi JR
• Park W

• KMID: 2223110
• DOI: http://doi.org/10.4078/jrd.2012.19.2.108

Abstract

Wegener's granulomatosis is an uncommon disease characterized by variable degrees of disseminated vasculitits involving both small arteries and veins. This disease is rarely associated with thrombosis. Isolated reports of intracranial thromboses of large and small vessels have been described in both adults and children. This report describes the first case of cortical vein thrombosis which was central nervous system manifestation in Wegener's granulomatosis.

Keyword

Cortical vein thrombosis; Wegener's granulomatosis

MeSH Terms

Adult
Arteries
Central Nervous System
Child
Humans
Intracranial Thrombosis
Thrombosis
Veins
Wegener Granulomatosis

Figure

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  Figure 1 (A) 14 days prior to the incident, the venous sinus occlusion CT imaging is normal. (B) Accident when the underlying, the venous sinus thrombosis.

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  Figure 2 (A) Right internal carotid artery angiography shows obstruction of right transverse sinus (arrow) and sigmoid sinus (small arrow) in venous phase, comparing normal left transverse sinus. (B) Right internal carotid arteriography shows total non-visualization in vein of Galen (arrow) and straight sinus (small arrow) and shows abnormal collateral vessels (white arrow) around the sinuses.

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