J Korean Ophthalmol Soc.  2012 Aug;53(8):1157-1162. 10.3341/jkos.2012.53.8.1157.

Scleral Window Surgery with Mitomycin C for Nanophthalmic Uveal Effusion: Case Report

• Kim SJ
• Kim GN
• Han YS
• Chung IY
• Seo SW
• Yoo JM
• Park JM

• KMID: 2215960
• DOI: http://doi.org/10.3341/jkos.2012.53.8.1157

Abstract

PURPOSE
To report the case of a 36-year-old patient with nanophthalmic uveal effusion was treated with scleral window surgery and topical administration of mitomycin C (MMC).
CASE SUMMARY
A 36-year-old woman presented with decreased visual acuity and blurred vision in the both eyes during 3 months. Fundus examination revealed choroidal effusion and retinal detachment with thickend sclera wall and short axial lengh. Partial-thickness sclera flap with deep sclerostomy was performed and topical MMC was administered to one quadrant of the equatorial sclera. The subretinal fluid resorbed gradually and visual acuity improved.
CONCLUSIONS
Scleral window surgery and topical mitomycin C might relieve the blocked transscleral outflow of intraocular fluid in the small area of a sclerostomy in young patient with nanophthlamos.

Keyword

Mitomycin C; Nanophthalmos; Scleral window surgery; Uveal effusion syndrome

MeSH Terms

Administration, Topical
Adult
Aqueous Humor
Choroid
Eye
Female
Humans
Mitomycin
Retinal Detachment
Sclera
Sclerostomy
Subretinal Fluid
Vision, Ocular
Visual Acuity
Mitomycin

Figure

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  Figure 1 Preoperative examination. Fundus photographs showed tortuous dilated retinal vessels and choroidal folding in the both eyes, and serous retinal detachment at left macular area (A and B). Fluorescein angiogram showed diffuse hyperfluorescence in the choroid that appeared in the early phase (C) and in the late phase, showed dye pooling in the left macular area (D). Central macular thikness checked by optical coherence tomography (OCT) were 370 µm in the right eye and 762 µm in the left eye (E).

• 

  Figure 2 Preoperative B-scan ultrasonography (A: right eye, B: left eye) and T2-weighted magnetic resonance image (C) showed small eyes, thicked sclera and thickened choroid, especially in the left eye.

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  Figure 3 Postoperative examination 2 years after sclera window surgery and topical administration of mitomycin C (MMC). Fundus photographs (A, B) and optical coherence tomography (C) showed no serous retinal detachment or choroidal folding C in the both eyes.

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