J Korean Ophthalmol Soc.  2015 Nov;56(11):1794-1797. 10.3341/jkos.2015.56.11.1794.

A Case of Steatocystoma Simplex of the Orbit

• Kim YJ
• Lee YS
• Chi MJ

• KMID: 2214190
• DOI: http://doi.org/10.3341/jkos.2015.56.11.1794

Abstract

PURPOSE
Steatocystoma is a cyst that originates embryologically from hair follicles and usually occurs on the face, chest, back and axillae as multiple lesions and rarely occurs as a solitary lesion. We experienced a case of steatocystoma simplex that developed in the orbit and present our case with a brief review of the literature.
CASE SUMMARY
A 44-year-old male presented with a history of palpable mass in the right inferomedial periorbital area that had been slowly growing for a few months. Physical examination revealed a non-tender, soft and round mass. Magnetic resonance imaging of the orbit showed 2.0 x 2.0 x 2.0 cm-sized mass in the right inferomedial orbit. We performed excisional biopsy of the orbital mass using transconjunctival approach. The pathological diagnosis was steatocystoma. There was no local recurrence during the postoperative follow-up.
CONCLUSIONS
We experienced a rare case of steatocystoma simplex that developed in the orbit. Base on our results, steatocystoma simplex should be considered when diagnosing an orbital mass.

Keyword

Orbital tumor; Solitary mass; Steatocystoma simplex

MeSH Terms

Adult
Axilla
Biopsy
Diagnosis
Follow-Up Studies
Hair Follicle
Humans
Magnetic Resonance Imaging
Male
Orbit*
Physical Examination
Recurrence
Thorax

Figure

• 

  Figure 1. 2.0 × 2.0 × 2.0 cm-sized, well defined mass at inferomedial portion of the right orbit on magnetic resonance (MR) images. The mass shows high signal intensity on T1-weighted coronal image (A) and T2-weighted axial image (B). Gadolinium-en-hanced T1-weighted fat-suppressed coronal image demonstrates non-enhancing mass.

• 

  Figure 2. Gross findings of the specimen. About 2.3× 2.0×1.8 cm-sized, round-shaped, well-demarcated mass is seen in the right inferomedial orbit.

• 

  Figure 3. Histological examination. (A) Histological examination reveals a folded, empty cyst lined by squamous epithelium and flattened sebaceous glands (black arrow) within the cyst wall (HE stain, ×40). (B) A thick, eosinophilic cuticle (red arrow) covers the surface of the epithelium (HE stain, ×100). HE = Hematoxylin-Eosin.

Reference

References

1. Brownstein MH. Steatocystoma simplex. A solitary steatocystoma. Arch Dermatol. 1982; 118:409–11.

2. Kim SH, Ahn BC. Steatocystoma simplex of the orbit. J Korean Ophthalmol Soc. 2000; 41:2000–2.

3. Kim TJ, Kim N, Park HJ. . A case of eyelid steatocystoma. J Korean Ophthalmol Soc. 2012; 53:1027–9.

4. Procianoy F, Golbert MB, Golbspan L. . Steatocystoma simplex of the eyelid. Ophthal Plast Reconstr Surg. 2009; 25:147–8.

5. Tirakunwichcha S, Vaivanijkul J. Steatocystoma simplex of the eyelid. Ophthal Plast Reconstr Surg. 2009; 25:49–50.

6. Kim NJ, Moon KC, Khwarg SI. Steatocystoma simplex of the caruncle. Can J Ophthalmol. 2006; 41:83–5.

7. Bowyer J, Sullivan T, Whitehead K. Steatocystoma simplex of the caruncle. Br J Ophthalmol. 2003; 87:240–1.

8. Stagner AM, Jakobiec FA, Yoon MK. Ruptured canthal steatocysto-ma simplex presenting as a lacrimal sac mass. Clin Experiment Ophthalmol. 2015; 43:385–7.