J Korean Ophthalmol Soc.  2009 Jul;50(7):1111-1114. 10.3341/jkos.2009.50.7.1111.

A Case of Bulbar Conjunctival Schwannoma

• Kim SU
• Gu MJ
• Lee JK
• Park DJ

• KMID: 2212503
• DOI: http://doi.org/10.3341/jkos.2009.50.7.1111

Abstract

PURPOSE
The schwannoma is a tumor originating from Schwann cell proliferation. Schwannoma is a rare disease, making up only 1% of all the tumors that develop in the orbit. Schwannomas usually arise from the choroids or the ciliary body, and occurrence in the conjunctiva is especially rare. Few cases have been reported worldwide, and no cases have been reported in Korea thus far. We report our case along with a literature review. CASE SUMMARY: A 31-year-old male patient visited our department with a history of discomfort of in his right eye for the past 5 years caused by a bulbar conjunctival mass. On ophthalmologic examination, a 5x3x3 mm, elevated, yellowish mass with a smooth surface was observed on the bulbar conjunctiva adjacent to the superonasal limbus near the 2 o'clock area of the right eye. We performed excision and biopsy for diagnosis and treatment of the bulbar conjunctival mass and confirmed the pathologic report for the diagnosis of schwannoma.

Keyword

Bulbar conjunctiva; Schwann cell; Schwannoma

MeSH Terms

Adult
Biopsy
Cell Proliferation
Choroid
Ciliary Body
Conjunctiva
Eye
Humans
Korea
Male
Neurilemmoma
Orbit
Rare Diseases

Figure

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  Figure 1. Right eye showing a smooth, well-circumscribed, elevated, yellow, bulbar conjunctival lesion.

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  Figure 2. Slit-lamp photograph at postoperative day 60 shows mild scar with vascularization.

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  Figure 3. Light microscopic findings. Tumor cells are fusiform and arranged in bundles in a fibrous stroma (hematoxylin-eosin, original magnification ×100 A, ×200 B).

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  Figure 4. Immunohistologic findings. (A) Strong expression of S-100 protein by tumor cells. The positive reaction is seen as a rust color. (B) No reactivity for HMB-45 antibody. (C) The reticulin stain shows abundant fibers within the tumor.

Reference

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