J Korean Ophthalmol Soc.  2009 May;50(5):790-793. 10.3341/jkos.2009.50.5.790.

A Case of Granular Cell Tumor in Form of Ciliary Body Tumor

• Ahn JH
• Seo SG
• Her J

• KMID: 2212326
• DOI: http://doi.org/10.3341/jkos.2009.50.5.790

Abstract

PURPOSE:To report a case of a granular cell tumor in the form of cilliary body tumor.
CASE SUMMARY
A 42-year-old women visited our clinic with blurred vision of the right eye, which began was 1 month earlier ago. Her medical history was unremarkable. Slit-lamp examination revealed a ciliary body tumor and complicated cataract due to a mass lesion. For treatment, an excisional biopsy of the ciliary body tumor and phacoemulsification were performed. The pathologic finding confirmed the diagnosis of a granular cell tumor. There was no evidence of a recurrent lesion of the tumor at the 6-month postoperative follow-up.
CONCLUSIONS
We confirmed a granular cell tumor in the form of a cilliary body tumor based on pathologic findings.

Keyword

Cilliary body tumor; Granular cell tumor

MeSH Terms

Adult
Biopsy
Cataract
Ciliary Body
Eye
Female
Follow-Up Studies
Granular Cell Tumor
Humans
Phacoemulsification
Vision, Ocular

Figure

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  Figure 1. Slitlamp photograph shows 0.4×0.4 cm-sized mass behind inferior iris.

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  Figure 2. Preoperative orbital CT finding. 0.5×0.5 sized well defined isodense mass lesion with intense enhancement in inferolateral aspect of right iris.

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  Figure 3. The tumor consist of sheet-like polygonal cells with glanular cytoplasmosis, and mitoses are rarely seen (H&E, ×100).

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  Figure 4. The tumor cells reveal potent reaction for S-100 protein (Immunohistochemical stain, ×100).

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  Figure 5. Tumor remnant was not seen, and IOL was positioned well on seven days postop.

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