J Korean Surg Soc.  2008 May;74(5):383-386.

Peutz-Jeghers Syndrome Associated with Jejuno- jenunal Intussusception

• An MS
• Kim WW
• Oh SH
• Lee NJ

Abstract

Peutz-Jeghers syndrome (PJS) is a rare hereditary disease where the clinical manifestations are multiple harmatomatous gastrointestinal polyps and pigmentations of the skin. A harmatomatous polyp can develop at any part of the gastrointestinal tract, and the proximal small bowel is frequently involved. Intestinal obstruction, bleeding and intussusception, caused by GI polyps have been reported, which often require repeated surgery. A female patient presented with suffering of abdominal pain for two days duration. The patient was diagnosed with intussusception, and a resection and anastomosis of the small bowel was performed. The patient was treated for 15 days, and was discharged from the hospital without any particular complications. We report this case with a review of the literature.

Keyword

Peutz-Jeghers syndrome; Intussusception

MeSH Terms

Abdominal Pain
Female
Gastrointestinal Tract
Genetic Diseases, Inborn
Hemorrhage
Humans
Intestinal Obstruction
Intussusception
Peutz-Jeghers Syndrome
Pigmentation
Polyps
Skin
Stress, Psychological