J Korean Soc Surg Hand.  2013 Jun;18(2):81-84. 10.12790/jkssh.2013.18.2.81.

Carpal Tunnel Syndrome in Congenital Radial Dysplasia

• Kim JY
• Gong GM
• Gwak HC
• Park DH
• Lee HJ

• KMID: 2194162
• DOI: http://doi.org/10.12790/jkssh.2013.18.2.81

Abstract

Congenital radial dysplasia is a rare disease with the defect or hypoplasia of radial side of forearm and hand. Congenital radial dysplasia is often accompanied by deformities of other parts. However, carpal tunnel syndrome caused by congenital radial dysplasia is very rare. We report one case of 53-year-old man with congenital radial dysplasia who underwent surgery for carpal tunnel syndrome.

Keyword

Congenital radial dysplasia; Carpal tunnel syndrome; Carpal tunnel release

MeSH Terms

Carpal Tunnel Syndrome
Congenital Abnormalities
Forearm
Hand
Rare Diseases

Figure

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  Fig. 1. Gross photograph of both hand. Severe thenar muscle atrophy is seen at right hand.

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  Fig. 2. Both wrist anteroposterior radiography and both wrist carpal tunnel view. Remnant of scaphoid is seen at adjacent radial process.

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  Fig. 3. Preoperative computed tomogram at level of the hook of hamate of the both wrist. The anteroposterior diameter and cross section area of the affected side (A) are smaller than those of unaffected side (B).

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  Fig. 4. Intraoperative finding of median nerve. Severe stenosis in carpal tunnel and compression median nerve just below retinaculum is noted.

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