J Korean Neurosurg Soc.  2016 May;59(3):197-203. 10.3340/jkns.2016.59.3.197.

Craniosynostosis in Growing Children : Pathophysiological Changes and Neurosurgical Problems

• Choi JW
• Lim SY
• Shin HJ

• KMID: 2192086
• DOI: http://doi.org/10.3340/jkns.2016.59.3.197

Abstract

Craniosynostosis is defined as the premature fusion of one or more cranial sutures resulting in skull deformity. Characteristically, this disorder can cause diverse neurosurgical problems, as well as abnormal skull shape. Intracranial hypertension, hydrocephalus, Chiari malformation and neuropsychological dysfunction are the major neurosurgical concerns in children with craniosynostosis. In this review article, we investigate pathophysiology, characteristics and proper neurosurgical management of these neurosurgical issues, respectively.

Keyword

Chiari Malformation; Craniosynostosis; Hydrocephalus; Intracranial hypertension; Neuropsychological

MeSH Terms

Child*
Congenital Abnormalities
Cranial Sutures
Craniosynostoses*
Humans
Hydrocephalus
Intracranial Hypertension
Skull

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