J Korean Neurosurg Soc.  2014 Jun;55(6):375-378. 10.3340/jkns.2014.55.6.375.

Endoscopic Coagulation of Choroid Plexus in Hydranencephaly

• Kim SY
• Cho JH
• Kim KH

• KMID: 2191121
• DOI: http://doi.org/10.3340/jkns.2014.55.6.375

Abstract

Hydranencephaly is a rare congenital disease defined as an absence of cerebral hemispheres with an intact thalamus, brain stem, and cerebellum. Generally, patients with hydranencephaly require cerebro-spinal fluid diversion due to progressive hydrocephalus. An excellent view of the choroid plexus and advancement of the neurosurgical endoscope were possible, leading to easy coagulation of the choroid plexus to balance cerebro-spinal fluid production without the use of a shunt device. We present this rare case and good treatment outcome from endoscopic coagulation of the choroid plexus.

Keyword

Hydranencephaly; Choroid plexus; Coagulation; Endoscope; Hydrocephalus

MeSH Terms

Brain Stem
Cerebellum
Cerebrum
Choroid Plexus*
Endoscopes
Humans
Hydranencephaly*
Hydrocephalus
Thalamus
Treatment Outcome

Figure

• 

  Fig. 1 CT scan shows an absence of cerebral hemispheres except a small portion of the occipital lobe. However, the thalami, brain stem, and cerebellum are preserved (A and B). Two choroid plexus between thalami are revealed on contrast CT scan (C).

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  Fig. 2 The choroid plexus before coagulation is observed on the thalami by endoscope (A). The choroid plexus became shrinkage and the blood flow of that was blocked after coagulation (B).

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  Fig. 3 The choroid plexus is not visible on contrast CT scan after 6 months, and other structures are revealed a similar findings to the preoperative imaging.

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