J Korean Neurosurg Soc.
1979 Sep;8(2):489-494.
A Case of Von Hippel-Lindau Disease
- Affiliations
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- 1Department of Neurosurgery, Yonsei University College of Medicine, Seoul, Korea.
Abstract
- The authors have experienced a case of Von Hippel-Lindau disease. A 31 year old man had angioma in the right retina and cystic capillary hemangioblastoma in the left cerebellar hemisphere. The retinal angioma was diagnosed by fundoscopic examination and the hemangioblastoma in the cerebellum was confirmed pathologically. The frequent associated disease, such as pheochromocytoma, polycythemia and intraabdominal tumor, was not noted clinically and radiologically. Total removal of the cerebellar tumor was performed with good result.