Allergy Asthma Immunol Res.  2012 May;4(3):165-167. 10.4168/aair.2012.4.3.165.

The First Probable Case of Hereditary Angioedema in Vietnam

• Bui Van K
• Nguyen Van D

• KMID: 2167070
• DOI: http://doi.org/10.4168/aair.2012.4.3.165

Abstract

Hereditary angioedema (HAE) is rare disorder due to C1-inhibitor deficiency (C1-INH) that are debilitating and may be life-threatening. HAE is a lack of consensus concerning diagnosis, therapy, and management, particularly in Vietnam. In this case report, we report a 40-year-old male patient with typical clinical symptoms and family history but he showed normal C4 level, and we could not measure C1q and C1-INH level. However, the diagnosis of HAE can be made based on typical clinical symptoms and the favorable prophylactic response to danazol treatment. Based on these findings, we suggest that he has type I HAE, although he showed normal C4 level.

Keyword

Hereditary angioedema; Vietnam

MeSH Terms

Adult
Angioedemas, Hereditary
Consensus
Danazol
Humans
Male
Vietnam
Danazol

Figure

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  Fig. 1 The swelling of the face.

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  Fig. 2 The swelling of the right hand.

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