Korean J Dermatol.  2016 Mar;54(3):206-209.

A Rare Cutaneous Presentation of Metastatic Orbital Adenocarcinoma

• Kim J
• Seo J
• Oh SH
• Kim SH
• Chung KY

Abstract

Primary ductal adenocarcinoma of the lacrimal gland (PDALG) is a rare tumor accounting for less than 2% of all tumors arising within the orbit. It is classified as a high-grade malignant epithelial tumor due to its variable biologic behavior and aggressive clinical course. Due to its rare incidence, the clinicopathologic profile is poorly identified and generally dependent on the few available reports and case series. Metastatic lesion of PDALG presenting as a skin lesion is very rare with only one previously reported case. We report here a case of metastatic PDALG that presented with cutaneous features. This case illustrates that such a rare malignant tumor may present to dermatologists, requiring prompt diagnosis and management with a multidisciplinary approach.

Keyword

Primary ductal adenocarcinoma of the lacrimal gland; Metastatic adenocarcinoma; Orbital adenocarcinoma

MeSH Terms

Adenocarcinoma*
Carcinoma
Diagnosis
Incidence
Lacrimal Apparatus
Orbit*
Skin