J Cardiovasc Ultrasound.  2016 Mar;24(1):75-78. 10.4250/jcu.2016.24.1.75.

A Case of Microangiopathic Hemolytic Anemia after Myxoma Excision and Mitral Valve Repair Presenting as Hemolytic Uremic Syndrome

• Park YJ
• Kim SP
• Shin HJ
• Choi JH

• KMID: 2161001
• DOI: http://doi.org/10.4250/jcu.2016.24.1.75

Abstract

Microangiopathic hemolytic anemia occurs in a diverse group of disorders, including thrombotic thrombocytopenic purpura, hemolytic uremic syndrome, and prosthetic cardiac valves. Hemolytic anemia also occurs as a rare complication after mitral valve repair. In this report, we describe a case of microangiopathic hemolytic anemia following myxoma excision and mitral valve repair, which was presented as hemolytic uremic syndrome.

Keyword

Hemolytic anemia; Hemolytic uremic syndrome; Mitral valve annuloplasty

MeSH Terms

Anemia, Hemolytic*
Heart Valves
Hemolytic-Uremic Syndrome*
Mitral Valve Annuloplasty
Mitral Valve*
Myxoma*
Purpura, Thrombotic Thrombocytopenic

Figure

• 

  Fig. 1 A transthoracic echocardiogram (A) and transesophageal echocardiogram (B) showed a huge (8.1 × 1.44 cm), highly mobile, echolucent, snake-shaped left atrial mass with moderate to severe eccentric mitral regurgitation.

• 

  Fig. 2 A peripheral blood smear showed red blood cell fragmentation with a few schistocytes (asterisk, 6/high power field) and polychromasia (arrow).

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  Fig. 3 The transthoracic echocardiogram showed moderate eccentric mitral regurgitation with multiple jet striking the annuloplasty ring.

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