Korean J Ophthalmol.  2016 Apr;30(2):151-153. 10.3341/kjo.2016.30.2.151.

Early Retinal Changes in Hunter Syndrome According to Spectral Domain Optical Coherence Tomography

• Kim S
• Yoo YJ
• Woo SJ
• Yang HK

• KMID: 2160468
• DOI: http://doi.org/10.3341/kjo.2016.30.2.151

Abstract

No abstract available.

MeSH Terms

Mucopolysaccharidosis II*
Retinaldehyde*
Tomography, Optical Coherence*
Retinaldehyde

Figure

• 

  Fig. 1 Slit lamp biomicroscopy showed clear corneas in the right (A) and left (B) eyes. (C,D) Comparison of spectral domain optical coherence tomography (SD-OCT; Spectralis, Heidelberg Engineering, Heidelberg, Germany) scans of the macula in early stage Hunter syndrome and normal control. (C) Vertical scan images with SD-OCT of the patient's right eye. There was marked thickening of the external limiting membrane (ELM). The ellipsoid zone (EZ) formerly known as the inner and outer segment photoreceptor junction appeared normal in thickness and contour, well distinguished from the retinal pigment epithelial layer underneath. The photoreceptor layer and retinal pigment epithelium-Bruch's membrane complex (RPE/Bruch's complex) showed no thinning or other abnormal change. (D) SD-OCT of the normal eye from a control subject showed four distinct high-signal bands in the outer retinal layer without foveal thickening of the ELM.

Reference

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