A Case of Primary Orbital Hemangioperycytoma

Lee, Sang Yong; Rho, Joo Heon

Abstract

Hemangiopericytoma is a rare tumor which originate from the soft tissue. The main sites are lower extremity, pelvic retroperitoneum and especially it is rare to occur primarily in the orbit. It is characterized that hemangiopericytoma possesses the potential of malignancy, but prediction of ultimate behavior is difficult because the clinical course often dose not coincide with histopathologic indicators of malignancy. We experienced a case of primary orbital hemagiopericytoma in a 31-yearold man who had complained diplopia and decreased vision, proptosis, downward and outward deviation of right eye. These symptoms had been occured 7 years ago. MRI examination demonstrated a well-defined tissue mass in superomedial extraconal space in the right orbit. We excised the tumor completely and found it was originated from the vessels with immunohistochemical study utilizing CD34 and Factor VIII-R-Ag as diagnostic marker. Also we confirmed the tumor is a hemangiopericytoma in the Gomoris reticulin stain and EM findings. No recurrence occured for more than 12 months after the initial complete excision. So we present our case with a brief review of the lietrature.