Korean J Dermatol.  2002 Jan;40(1):92-94.

A Case of Pityriasis Rubra Pilaris in an Infant

• Lim TG
• Lee SJ
• Kim YK
• Choi GS

Abstract

Pityriasis rubra pilaris is a rare papulosquamous and keratotic disease. The orange hue to the erythema, the thickening of the palms and soles and so called 'islands of normal skin' contribute to establish the diagnosis based on morphologic features. We present a 6-month-old male patient with multiple scaly erythematous patches and 'island of normal skin' on the face. There is no palmoplantar keratoderma, nor onychopathy. Histopathologic findings revealed alternating parakeratosis and hypergranulosis in the epidermis and mild perivascular lymphocytic infiltration in the dermis. Unlike to Griffiths classification, he showed good responses to topical steroid and UV phototherapy.

Keyword

Pityriasis rubra pilaris; Infant

MeSH Terms

Citrus sinensis
Classification
Dermis
Diagnosis
Epidermis
Erythema
Humans
Infant*
Keratoderma, Palmoplantar
Male
Parakeratosis
Phototherapy
Pityriasis Rubra Pilaris*
Pityriasis*