J Cardiovasc Ultrasound.  2011 Mar;19(1):32-34. 10.4250/jcu.2011.19.1.32.

A Case of Right Sided Aortic Arch Combined with Atrial Septal Defect

• Ha GJ
• Sung MJ
• Lee YS
• Lee JB
• Ryu JK
• Lee S
• Choi JY
• Kwon OC
• Chang SG
• Kim KS

• KMID: 2135430
• DOI: http://doi.org/10.4250/jcu.2011.19.1.32

Abstract

Right sided aortic arch is an uncommon congenital anomaly. It can be classified into three types, depending on the left aortic arch's degenerating pattern and the branching pattern of the great vessels. It can be associated with major congenital heart disease, depending on the type of right sided aortic arch. We report a case of an 18-years-old female who has right sided aortic arch with atrial septal defect (ASD). In our case, the patient had a right sided aortic arch and aberrant left subclavian artery, also she had ASD (ostium secundum) and moderate tricuspid regurgitation with pulmonary hypertension. The patient was successfully performed patch closure of ASD and tricuspid valve annuloplasty via midline sternotomy. The patient had uneventful postoperative course.

Keyword

Right sided aortic arch; Atrial septal defect

MeSH Terms

Aneurysm
Aorta, Thoracic
Cardiovascular Abnormalities
Deglutition Disorders
Female
Heart Diseases
Heart Septal Defects, Atrial
Humans
Hypertension, Pulmonary
Sternotomy
Subclavian Artery
Tricuspid Valve
Tricuspid Valve Insufficiency
Aneurysm
Cardiovascular Abnormalities
Deglutition Disorders
Subclavian Artery

Figure

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  Fig. 1 Chest X-ray showed mild cardiomegaly and increased pulmonary vascularity in both lungs.

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  Fig. 2 Transthoracic echocardiography showed a large atrial septal defect (arrow), ostium secundum type (32-38 mm).

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  Fig. 3 Chest dynamic computed tomography showed right sided aortic arch (arrow).

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  Fig. 4 Chest dynamic computed tomography showed the great vessels originated from the arch in the following order, left common carotid artery (right arrow) (A), right common carotid artery (left arrow) (A), right subclavian artery (B), and aberrant left subclavian artery (C). Left subclavian artery originated from descending aortic arch.

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