J Korean Cleft Palate-Craniofac Assoc.  2005 Apr;6(1):69-72.

Treatment of Pan-craniofacial Polyostotic Fibrodysplasia not Involving Maxilla: Mandible Reconstruction with Free Fibular Bone Flap

• Cheon SJ
• Lee KS

Abstract

Fibrous dysplasia is a benign pathologic condition of bone and causes facial deformity as well as functional problems. The monostotic form of the disease is much more common(70-80 percent) than the polyostotic variety (20-30 percent). In craniofacial fibrous dysplasia, craniofacial involvement occurs in 10-30 percent of monostotic and 50 percent of polyostotic patients. Frontal, sphenoid, ethmoid, and maxilla bones are frequently involved. Jaw involvement may involve a solitary lesion, but nonetheless in more common in the maxilla than in the mandible. We report a case of mandible reconstruction of pan-craniofacial polyostotic fibrous dysplasia that do not involve maxilla. In operation, extensive hemimandibulectomy was done and fibular bone free flap was done for mandible reconstruction. Postoperative 6 months later, focal osteomyelitis was seen in mandible angle. We removed mini-plate and screw and illiac cancellous bone graft was performed. 3 months after second operation, wound healing was uneventful and we have a functionally and cosmetically good outcome.

Keyword

Fibrous dysplasia; Mandible reconstruction; Fibular bone free flap

MeSH Terms

Congenital Abnormalities
Fibrous Dysplasia, Polyostotic
Free Tissue Flaps
Humans
Jaw
Mandible*
Mandibular Osteotomy
Maxilla*
Osteomyelitis
Transplants
Wound Healing