Brain Tumor Res Treat.  2015 Oct;3(2):115-117. 10.14791/btrt.2015.3.2.115.

Aneurysmal Bone Cyst of Sphenoid Bone and Clivus Misdiagnosed as Chordoma: A Case Report

• Ustabasioglu FE
• Samanci C
• Asik M
• Yanik I
• Ozkanli S
• Tutar O
• Hasiloglu

• KMID: 2114657
• DOI: http://doi.org/10.14791/btrt.2015.3.2.115

Abstract

Aneurysmal bone cysts (ABCs) are benign and rapidly expanding bone destructive lesions of any bone. They are commonly localized in the metaphysis of long bones, whereas skull base ABCs are rare. We report a case of a 21-year-old man who had been misdiagnosed as chordoma and undergone surgery. However, histopathological examination revealed it to be an ABC.

Keyword

Bone cyst, aneurysmal; Chordoma; Magnetic resonance imaging

MeSH Terms

Aneurysm*
Bone Cysts*
Bone Cysts, Aneurysmal
Chordoma*
Cranial Fossa, Posterior*
Humans
Magnetic Resonance Imaging
Skull Base
Sphenoid Bone*
Young Adult

Figure

• 

  Fig. 1 Preoperative axial T2-weighted image (A) of the skull base revealed multiple multiloculated fluid-fluid cavities with hemorrhagic areas are consistent with associated aneurysmal bone cysts. T1-weighted, post-contrast, fat suppressed sagittal (B) and coronal (C) MR images and T1-weighted, pre (D) and post-contrast (E), fat suppressed sagittal MR images demonstrating heterogeneous enhancement of the solid components of the lesion.

• 

  Fig. 2 A: Histological features composed of haemorrhagic spaces of blood-filled cavities. B: These cavities are surrounded by fibrotic septa, inflammatory cells and osteoclast cells that are distributed around the cystic spaces (hematoxylin and eosin).

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