J Korean Soc Transplant.  1999 Dec;13(2):323-328.

Radical Resection of Inferior Vena Cava Leiomyosarcoma; Hepatic and IVC Resection with Vascular Reconstruction and Kidney Autotransplantation

• Joh JW
• Kim SJ
• Choi IS
• Heo JS
• Lim SW
• Kim YI
• Lee BB

Abstract

Malignant sarcomas arising from the wall of blood vessels are extremely rare. It tends to enlarge by intra- or extra-luminal extension rather than infiltration, in some instances the tumor origin from the IVC invaded adjacent vital structures limit the extent of the resection. However, a wide and complete surgical resection provided the best chance for prolonged survival in patients. We experienced one case of IVC tumor invaded to right renal vein and liver. In a 52-year-old women suffering right frank pain, right upper retroperitoneal mass was found. In preoperative CT, MRI, Vena Cavogram, the mass was invaded to the right and quadate lobe of the liver, adrenal gland, and right renal vein. We performed the en-block resection including the right hepatic and quadate lobe, IVC and both kidney, and then IVC was reconstructed with graft (PTFE) and uninvolved left kidney was autotransplanted at right peritoneal space. Postoperatively, the patient was recovered satisfactory without complication. Because only way of preventing the development of recurrence is the radical resection of the IVC tumor including adjacent organs, a preoperative accurate staging and aggressive treatment are recommended.

Keyword

IVC leiomyosarcoma; Radical resection

MeSH Terms

Adrenal Glands
Autografts*
Blood Vessels
Female
Humans
Kidney*
Leiomyosarcoma*
Liver
Magnetic Resonance Imaging
Middle Aged
Recurrence
Renal Veins
Sarcoma
Transplants
Vena Cava, Inferior*