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J Korean Surg Soc.  2010 Dec;79(6):503-507. 10.4174/jkss.2010.79.6.503.

Dermatofibrosarcoma Protuberans in Abdominal Wall Aggravated during Pregnancy

Affiliations
  • 1Department of Surgery, Seoul National University Boramae Hospital, Seoul, Korea. jkchung@brm.co.kr
  • 2Department of Pathology, Seoul National University Boramae Hospital, Seoul, Korea.
  • 3Department of Obstetrics and Gynecology, Seoul National University Boramae Hospital, Seoul, Korea.

Abstract

Dermatofibrosarcoma protuberans is a rare tumor that occurs in the dermis or subcutaneous tissue of the trunk or extremities in relatively young adults. There are few reports of Dermatofibrosarcoma protuberans associated with pregnancy. We experienced a 28-year-old pregnant female patient with an abdominal wall mass, which grew rapidly during pregnancy. Excisional biopsy was performed and the pathologic diagnosis was fibrosarcoma transformed from Dermatofibrosarcoma protuberans. Dermatofibrosarcoma protuberans showed a positive CD34 immunostaining while fibrosarcoma showed a negative CD34. There was no recurrence or metastasis with the follow up period of 2 years. We report here a rare case of Dermatofibrosarcoma protuberans aggravated during pregnancy with a review of the literature.

Keyword

Abdominal wall; Dermatofibrosarcoma; Pregnancy

MeSH Terms

Abdominal Wall
Adult
Biopsy
Dermatofibrosarcoma
Dermis
Extremities
Female
Fibrosarcoma
Follow-Up Studies
Humans
Neoplasm Metastasis
Pregnancy
Recurrence
Subcutaneous Tissue
Young Adult
Dermatofibrosarcoma
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