Korean J Dermatol.  2003 Nov;41(11):1564-1567.

A Case of Linear and Whorled Nevoid Hypermelanosis Associated with Congenital Hemihypertrophy

• Yang JS
• Bae EY
• Park YM
• Kim HO
• Kim CW

Abstract

Linear and whorled nevoid hypermelanosis(LWNH) is a congenital disorder characterized by hyperpigmented macules in a linear and whorled pattern along Blaschko's lines, and develops a few weeks after birth. Skin manifestations closely resemble hypomelanosis of Ito with inverse pigmentation. There is no preceding inflammatory event and no pigmentary incontinence histologically. It may be associated with various congenital abnormalities. We report a case of linear and whorled nevoid hypermelanosis associated with congenital hemihypertrophy of left extremities in a 10-year old boy.

Keyword

Linear and whorled nevoid hypermelanosis; Congenital hemihypertrophy

MeSH Terms

Child
Congenital Abnormalities
Congenital, Hereditary, and Neonatal Diseases and Abnormalities
Extremities
Humans
Hyperpigmentation*
Hypopigmentation
Male
Parturition
Pigmentation
Skin Manifestations