J Adv Prosthodont.  2015 Oct;7(5):406-410. 10.4047/jap.2015.7.5.406.

Prosthetic management of a growing patient with Russell-Silver syndrome: a clinical report

• Kim K
• Noh K
• Paek J
• Kwon KR
• Pae A

• KMID: 2083885
• DOI: http://doi.org/10.4047/jap.2015.7.5.406

Abstract

Russell-Silver syndrome (RSS) is a congenital disease characterized by short stature due to growth hormone deficiency, physical asymmetry, inverted triangular face, micrognathia, prominent forehead, and hypodontia. This case report presents a prosthetic management of a 6-year-old patient with Russell-Silver syndrome treated with overdentures on the maxilla and the mandible using the remaining primary teeth. Subsequent and comprehensive dental management considering the growth and development of a young patient will be necessary.

Keyword

Russell-Silver syndrome; Hypodontia; Overdenture; Early prosthetic rehabilitation

MeSH Terms

Anodontia
Child
Denture, Overlay
Forehead
Growth and Development
Growth Hormone
Humans
Mandible
Maxilla
Silver-Russell Syndrome*
Tooth, Deciduous
Growth Hormone

Figure

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  Fig. 1 Pretreatment intraoral frontal view. Severe dental caries and multiple loss of primary teeth were presented.

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  Fig. 2 Pretreatment (A) extraoral frontal view, (B) extraoral lateral view, and (C) panoramic view. Typical craniofacial characteristics of RSS patient.

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  Fig. 3 Postextraction intraoral frontal view.

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  Fig. 4 Definitive cast after border molding and final impression making for (A) maxillary and (B) mandibular overdenture.

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  Fig. 5 Arrangement of prosthetic teeth on wax denture (A) with gingiva formation considering patient's young age, (B) developmental spaces, and tooth axis arranged vertical to occlusal plane.

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  Fig. 6 Posttreatment (A) extraoral lateral view showing satisfactory esthetic results and (B) panoramic view with definitive prostheses.

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  Fig. 7 Patient showing good adaptation to definitive prostheses.

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