Korean J Perinatol.  2013 Dec;24(4):306-309. 10.14734/kjp.2013.24.4.306.

Lumbocostovertebral Syndrome with Congenital Bilateral Lumbar Hernia

• Choi JW
• Cho HJ
• Na YH
• Kim MH
• Lim BK

• KMID: 2072308
• DOI: http://doi.org/10.14734/kjp.2013.24.4.306

Abstract

Lumbocostovertebral syndrome is a rare type of congenital lumbar hernia. Its features include lumbar hernia associated with genitourinary, vertebral, and rib anomalies. About 30 cases have been reported in the English literature, but in Korea, there has not been a case reported. We experienced a neonate with multiple costovertebral anomalies and bilateral lumbar hernia with liver and small intestine herniation diagnosed by physical examination and computed tomography. We report a case of a congenital lumbocostovertebral syndrome in neonate with literature review.

Keyword

Congenital lumbar hernia; Lumbocostovertebral syndrome

MeSH Terms

Hernia*
Humans
Infant, Newborn
Intestine, Small
Korea
Liver
Physical Examination
Ribs

Figure

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  Fig. 1 Burging mass at the both flank area.

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  Fig. 2 Chest X-ray show lumbar hernia and T9-T12 hemivertebrae, laterlization and caudalization of both lower rib.

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  Fig. 3 Abdomen CT showing bilateral oblique muscle defect with herniation of liver and bowel.

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  Fig. 4 Abdomen CT showing urachus.

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  Fig. 5 Chest CT showinghemivertebrae on T9-T12.

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