Korean J Anesthesiol.  2010 Jun;58(6):555-559. 10.4097/kjae.2010.58.6.555.

Rupture of abdominal aortic aneurysm after spine surgery in the patient with Ehlers-Danlos syndrome: A case report

• Im JS
• Lim YH
• Park JS
• Lee SS
• Kim KM

• KMID: 2031698
• DOI: http://doi.org/10.4097/kjae.2010.58.6.555

Abstract

Ehlers-Danlos syndrome (EDS) is a rare inherited disorder of the connective tissue that is characterized by hyperextensible skin, hypermobile joints and abnormalities of the cardiovascular system. A 15-year-old girl with Ehlers-Danlos syndrome underwent thoracolumbar surgery for deformity correction. After surgery, an abdominal aortic rupture occurred, and she complained of abdominal distension had an abdominal circumference of 80 cm. Abdominal computed tomography revealed a pseudoaneurysm and a large hematoma at the retroperitoneum. She died of a massive hemorrhage during subsequent abdominal aortic surgery.

Keyword

Abdominal aorta rupture; Ehlers-Danlos syndrome; Hemorrhage

MeSH Terms

Adolescent
Aneurysm, False
Aortic Aneurysm, Abdominal
Aortic Rupture
Cardiovascular System
Congenital Abnormalities
Connective Tissue
Ehlers-Danlos Syndrome
Hematoma
Hemorrhage
Humans
Joints
Rupture
Skin
Spine