J Korean Neurol Assoc.
1991 Mar;9(1):101-106.
Idiopathic Familial Intracerebral Calcification with Pyramidal Tract Degeneration
- Affiliations
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- 1Department of Neurology, Yonsei University, Korea.
- 2Department of Neurology, Ulsan University, Asan Medical Center, Korea.
Abstract
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A l9-year-old boy was admitted because of progressive spastic quadriparesis and bulbar palsy which developed from 3 years ago. The results of all performed laboratory tests were normal, but neuroradiologic tests revealed intracerebral calcification and degeneration of oilateral pyramidal tracts. Idiopathic familial intracerebral calcification was rarely occurred and presented usually with various extrapyramidal and cortical symptoms. Mild pyramidal symptoms were also associated in some reported cases, but none of them showed predominant spasticity as well as suspicious pyramidal tract degeneration on magnetic resonance imaging.