Korean J Hematol.
2003 May;38(2):142-146.
A Case of POEMS Syndrome with Unclassifiable Myeloproliferative Disorder
- Affiliations
-
- 1Department of Laboratory Medicine, Pundang Jesaeng General Hospital, Sungnam, Korea. hskim@dmc.or.kr
- 2Department of Neurology, Pundang Jesaeng General Hospital, Sungnam, Korea.
- 3Department of Internal Medicine, Pundang Jesaeng General Hospital, Sungnam, Korea.
Abstract
- POEMS syndrome is a rare multisystemic syndrome characterized by polyneuropathy, organomegaly, endocrinopathy, monoclonal gammopathy, and skin changes. We report a case of POEMS syndrome associated with unclassifiable myeloproliferative disorder presenting with polyneuropathy, hepatosplenomegaly, hypothyroidism, hyperprolactinemia, monoclonal gammopathy, hyperpigmentation, hypertrichosis, ascites, peripheral edema, and pulmonary hypertension.