Korean J Pathol.
2012 Dec;46(6):583-586.
Rosai-Dorfman Disease: Report of a Case Associated with IgG4-Related Sclerotic Lesions
- Affiliations
-
- 1Department of Pathology, Asan Medical Center, University of Ulsan College of Medicine, Seoul, Korea. jrhuh@amc.seoul.kr
- 2Department of Gastroenterology, Asan Medical Center, University of Ulsan College of Medicine, Seoul, Korea.
- 3Department of Pulmonology and Critical Care Medicine, Asan Medical Center, University of Ulsan College of Medicine, Seoul, Korea.
Abstract
- We describe a rare case of sinus histiocytosis with massive lymphadenopathy (Rosai-Dorfman disease) associated with a six-year history of autoimmune pancreatitis, which was controlled by steroid treatment. The patient presented with multiple, cervical and thoracic lymphadenopathy and abnormal, nodular opacities in the lung. Histologically, Rosai-Dorfman disease with numerous IgG4-positive cells was identified in a subcutaneous lymph node in the patient's left forearm. The patient recovered uneventfully with steroid treatment.
- Full Text Links
-
- Actions
-
Cited
- CITED
-
- Close
- Share
-
- Similar articles
-
- A Case of Cutaneous Rosai-Dorfman Disease Enlarged in Size after Punch Biopsy
- Rosai-Dorfman Disease in the Neck and Subglottis
- A Case of Rosai-Dorfman Disease Limited to the Lip
- Rosai-Dorfman Disease in the Breast with Increased IgG4 Expressing Plasma Cells: A Case Report
- Rapidly Growing Cutaneous Rosai-Dorfman Disease Successfully Treated with Surgical Excision
