Clin Pediatr Hematol Oncol.
2009 Oct;16(2):151-154.
A Case of Mesenteric Diffuse Lipoblastomatosis
- Affiliations
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- 1Department of Pediatrics, Pusan National University School of Medicine, Yangsan, Korea. limyt@pusan.ac.kr
- 2Department of Pathology, Pusan National University School of Medicine, Yangsan, Korea.
- 3Department of Surgery, Pusan National University School of Medicine, Yangsan, Korea.
Abstract
- Lipoblastoma is a uncommon benign neoplasm of embryonal fat that occurs typically in infancy and childhood. Most of these tumors present as a rapidly enlarging mass and are primarily located in the soft tissues of the extremities or trunk. Although more than 200 lipoblastomas have been reported, only 15 arose in the bowel mesentery, representing less than 7% of all lipoblastomas. The treatment of choice for mesenteric lipoblastomas is surgery. It has an excellent prognosis and does not behave aggressively or metastasize, but its growth is rapid. We report a case of mesenteric lipoblastomatosis in a 12-month-old child who had abdominal distension.