Korean J Pediatr.
2006 Feb;49(2):203-207. 10.3345/kjp.2006.49.2.203.
Gastric neurofibroma in von Recklinghausen disease: a cause of upper gastrointestinal bleeding
- Affiliations
-
- 1Department of Pediatrics, Seoul National University College of Medicine, Seoul, Korea. jkseo@snu.ac.kr
- 2Department of Surgery, Seoul National University College of Medicine, Seoul, Korea.
- 3Department of Radiology, Seoul National University College of Medicine, Seoul, Korea.
- 4Department of Pathology, Seoul National University College of Medicine, Seoul, Korea.
- KMID: 1966615
- DOI: http://doi.org/10.3345/kjp.2006.49.2.203
Abstract
- Neurofibromatosis type 1 (von Recklinghausen disease, NF1) involves the central and peripheral nervous systems as well as the skin, bone, endocrine, gastrointestinal and vascular systems. The gastrointestinal neurofibroma associated with NF1 has been infrequently reported. We report our experience with a 15-year-old boy who had a gastric plexiform neurofibroma with upper gastrointestinal bleeding and underwent a tumorectomy because of massive upper gastrointestinal bleeding. We conclude that gastrointestinal bleeding and anemia in the setting of NF1 mandates complete endoscopic examination of the digestive tract to rule out neurofibromas. Surgical resection is the standard treatment.
- Full Text Links
-
- Actions
-
Cited
- CITED
-
- Close
- Share
-
- Similar articles
-
- Diffuse Ganglioneuromatosis of Appendix associated with Von Recklinghausen;s Disease
- Solitary Plexiform Neurofibroma on the Median Nerve: A Case Report
- A Sudden Death in a Patient with Neurofibromatosis
- Von Recklinghausen' s Disease with Plexiform Neurofibroma , Giant Pigmentation , and Skeletal Abnormalities
- A Case of Cutaneous Neurofibroma Intimately Contacted with Intrathoracic and Chest Wall Plexiform Neurofibroma in Von Recklinghausen's Disease
