Korean J Pathol.  2007 Oct;41(5):334-336.

Diffuse Ganglioneuromatosis of Appendix associated with Von Recklinghausen;s Disease

Affiliations
  • 1Department of Pathology, Kyungpook National University School of Medicine, Daegu, Korea. baehi@knu.ac.kr

Abstract

Gastrointestinal ganglioneuromatosis is a rare neoplastic condition that can occur in association with von Recklinghausen's disease with multiple endocrine neoplasia type II B. The main locations are the ileum, colon, and appendix. We report a case of diffuse ganglioneuromatosis of the appendix associated with a mesenteric and ileocecal plexiform neurofibroma in von Recklinghausen's disease.

Keyword

Ganglioneuromatosis; Appendix; Von Recklinghausen's disease

MeSH Terms

Appendix*
Colon
Ileum
Multiple Endocrine Neoplasia
Neurofibroma, Plexiform
Neurofibromatosis 1
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