J Korean Assoc Maxillofac Plast Reconstr Surg.  1999 Nov;21(4):407-413.

A case report of neurocristopathy that shows oblique facial cleft, maxillary duplication and other facial malf ormations

Affiliations
  • 1Department of Oral and Maxillofacial Surgery, College of Dentistry, Kyung Hee University, Korea. omshome@khmc.or.kr

Abstract

Maxillary duplication is a kind of proliferative neurocristopathy and considered to arise from bifurcation of neural crest elements soon after their migration into mandibular arch. Sometimes this malformation is accompanied with oblique facial cleft. Usually this type of maxillofacial malformation requires multiple surgical intervention and the results are far from ideal. It became more troublesome if it had not been properly corrected on time, because secondary deformities could be developed from growth and development of abnormal tissues. This is a case of a 25-year-old-female patient who showed severe facial asymmetry thought to secondary deformity of maxillary duplication and masticatory disturbance due to multiple supernumerary teeth on posterior part right maxilla. We successully treated these deformities through four times of surgery of bone resection, orthodontic treatment, zygomatic and orbital reconstruction, orthognathic surgery and scar revision...ect. So we reported this rare case with review of literatures.

Keyword

Neurocristopathy; Facial cleft; Maxillary duplication

MeSH Terms

Cicatrix
Congenital Abnormalities
Facial Asymmetry
Growth and Development
Humans
Maxilla
Neural Crest
Orbit
Orthognathic Surgery
Tooth, Supernumerary
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