J Korean Neurol Assoc.
1990 Dec;8(2):389-392.
Two Families of Diunally Fluctuating Hereditary
Progressive Dystonia
- Affiliations
-
- 1Department of Neurology, Dong-A University, Korea.
- 2Department of Neurology, Seoul National University, Korea.
Abstract
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Diurnally fluctuating hereditary progessive dystonia is a rare movement disorder characterized by marked diurnal fluctuation of symptoms and dramatic response to levodopa. We report two advanced female patients of two families who presented with progressive dystonia and gait disturbance. Both patients have a family history and showed excellent response to levodopa.